Cystic fibrosis is a systemic hereditary disease in which a mutation of the protein involved in the transport of chlorine ions through the cell membrane arises, resulting in disturbances in the work of the glands of external secretion. These glands secrete mucus and sweat. Slime produced by glands of external secretion plays a very large role, this substance is necessary for moistening and protecting individual organs from drying out and infecting harmful bacteria, which is a mechanical barrier.
Cystic fibrosis is a disease caused by a defect of a single gene that controls the movement of salts in the body. The gene of cystic fibrosis is located in 7 pairs of chromosomes, and for the development of the disease, it is necessary that the child obtain this gene from both parents.
In cystic fibrosis, the mucus becomes dense and sticky, it accumulates in the excretory ducts of the bronchi, the pancreas and clogs them. This leads to the multiplication of bacteria, as the purifying function disappears. This disease is also called cystic fibrosis due to the development of cysts at the site of the ducts and glands. Cystic fibrosis affects mainly organs such as the lungs, pancreas, intestines, paranasal sinuses.
Antibacterial drugs are the main means of combating pulmonary infection. In this pathology, various groups are used (cephalosporins 2 to 3 generations, respiratory fluoroquinolones). Taking medications internally is used to treat mild infections. Inhalation antibiotics can be used to prevent or control infections caused by Pseudomonas bacteria.
Anti-inflammatory drugs can help reduce the swelling of the airways due to a long-lasting infection. The bronchodilators affect the lumen of the bronchi and help relax the bronchial muscles. Inhalation treatment often uses this group of drugs. With the development of a more severe degree, oxygen therapy may be necessary. This treatment is carried out with the help of mask oxygen.